Abstract: Objective: To analyze the quality of life status and influencing factors of adult patients with Pulmonary Hypertension (PH), and to provide a reference for the construction of targeted quality of life intervention programs. Methods: A total of 247 PH patients who visited the department of cardiology of a tertiary grade A hospital in Jinan from July 2021 to February 2022 were selected as subjects by convenience sampling method. The General Data Questionnaire, the World Health Organization Quality of Life Questionnaire, the Chinese version of the Simplified Fear Disease Progression Scale, the Perceptive Social Support Scale, and the simplified Chinese version of the Family Resilience Rating Scale were used to survey. Results: The average quality of life score of PH patients was 46.55±10.46 and the scores in four domains were lower than the norm. The results of stratified linear regression showed that the cardiac function, per capita monthly household income, fear of disease progression, perceived social support and family resilience were influencing factors of the quality of life of PH patients (P<0.05). Conclusion: The quality of life of PH patients is seriously impaired. Medical staff should pay more attention to PH patients with poor cardiac function, lower income, and fear of disease progression, help them develop positive and correct disease perception, improve social support and help their families to leverage the inherent advantages and strength, to improve the health level and quality of life of PH patients.

Key words: Pulmonary Hypertension; quality of life; influencing factor; fear of progression